Computed Tomographical Characterisation of Dyke-Davidoff-Masson Syndrome: A Case Series

Abstract

Dyke-Davidoff-Masson Syndrome (DDMS) is a rare neurological disorder that primarily manifests through various neurological symptoms, with a significant focus on contralateral hemiparesis and convulsive disorders that often show resistance to standard treatments. It is mainly characterised by hemicerebral atrophy, bony calvarial thickening and hyperpneumatisation of the ipsilateral paranasal sinuses on imaging. Computed Tomography (CT) is a crucial diagnostic tool in settings with limited resources, offering an effective means to identify and diagnose this syndrome. In the present paper, the authors present case reports of three patients (2 females, 1 male) with seizure disorders and hemiparesis who were admitted to the Medicine Department and had CT brain imaging performed within six months. The objective to highlight the diagnostic process and discuss the clinical presentation of this syndrome in a limited-resource setting, emphasising the role of CT in aiding diagnosis and further medical management.

Keywords

• convulsion
• computed tomography
• hemiatrophy
• hemiparesis
• porencephalic cyst
• seizure